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Abstract & Commentary
By Michael Rubin, MD , Professor of Clinical Neurology, Weill Cornell Medical College. Dr. Rubin reports no financial relationships relevant to this field of study.
Synopsis: Camptocormia may occur in a wide variety of central and peripheral nervous system disorders, including primary muscle disease.
Source: Margraf NG, et al. Camptocormia in idiopathic Parkinson's disease: A focal myopathy of the paravertebral muscles. Mov Disord (wiley.com. DOI: 10.1002/mds.22780).
Camptocormia (CC), abnormal trunk flexion appearing when standing or walking and disappearing when supine, has been attributed to normal aging, and a wide variety if disorders, including hysteria, spondylitis, neuromuscular disorders extending from the anterior horn cell to muscle including amyotrophic lateral sclerosis, myasthenia gravis, polymyositis, inclusion body myositis, and nemaline myopathy, to paraneoplasia, and valproate toxicity. Seen commonly in movement disorders, particularly Parkinson's disease (PD), it has been ascribed to axial dystonia. 1 Current evidence suggests that camptocormia in idiopathic PD may be myopathic in origin.
Between 2004 and 2007, 15 PD patients with CC and 15 without CC underwent comparison study encompassing detailed...